Upwardly displaced cervical aortic arch (CAA) is an uncommon congenital anomaly. In approximately 20% of cases, it includes an arch aneurysm which is most often situated between the origins of the left common carotid and subclavian arteries. While CAA alone is generally asymptomatic, dysphagia, dyspnea, and recurrent pulmonary infections can occur when an aneurysm is present. We report the surgical repair of a CAA and aneurysm in a 19-year-old male. The left aorta and the descending thoracic aorta were replaced under direct vision without complications, and the patient was discharged on postoperative day 10.